Nodal extramedullary hematopoiesis and facial bone change in thalassemia.
نویسندگان
چکیده
A 24-year-old regularly transfused patient with b-thalassemia major presented with a lateral neck mass. Computed tomography and magnetic resonance imaging showed an enhanced mass 2.3 3 2 3 2.2 cm in the right parotid gland (panels A-B, arrows) with expansion and coarsening of the bony parts (panel A, arrowheads). Differential diagnosis included salivary gland tumors, metastases, hematomas, hemangioma, and extramedullary hematopoiesis (EMH). Fine-needle aspiration of the mass showed normal bone marrow elements (panel C), and EMH was suggested. Pathology showed a soft, dark red, clot-like mass (panel D) that was confirmed as nodal EMH (panels E-F).
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ورودعنوان ژورنال:
- Blood
دوره 126 17 شماره
صفحات -
تاریخ انتشار 2015